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DeCS
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Descriptor English:
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POEMS Syndrome
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Descriptor Spanish:
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síndrome POEMS
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Descriptor Portuguese:
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Síndrome POEMS
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Synonyms English:
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Crow Fukase Syndrome
Crow-Fukase Syndrome
Organomegalies, Polyneuropathy
Organomegaly, Polyneuropathy
Polyneuropathy Organomegalies
Polyneuropathy Organomegaly
Polyneuropathy, Organomegaly, Endocrinopathy, M Protein, and Skin Changes Syndrome
Syndrome, Crow-Fukase
Syndrome, POEMS
Syndrome, Takatsuki's
Takatsuki Syndrome
Takatsuki's Syndrome
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Tree Number:
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C10.668.829.800.700
C15.378.147.780.750
C16.131.077.703
C20.683.780.750
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Definition English:
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A multisystemic disorder characterized by a sensorimotor polyneuropathy (POLYNEUROPATHIES), organomegaly, endocrinopathy, monoclonal gammopathy, and pigmentary skin changes. Other clinical features which may be present include EDEMA; CACHEXIA; microangiopathic glomerulopathy; pulmonary hypertension (HYPERTENSION, PULMONARY); cutaneous necrosis; THROMBOCYTOSIS; and POLYCYTHEMIA. This disorder is frequently associated with osteosclerotic myeloma. (From Adams et al., Principles of Neurology, 6th ed, p1335; Rev Med Interne 1997;18(7):553-62) |
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History Note English:
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1992
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Allowable Qualifiers English:
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Record Number:
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29882
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Unique Identifier:
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D016878
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Occurrence in VHL:
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Similar:
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DeCS
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